Int J Cardiovasc Imaging. 2026 Mar 9. doi: 10.1007/s10554-026-03670-4. Online ahead of print.
ABSTRACT
Desmoplakin (DSP) cardiomyopathy is an inherited condition caused by desmosome gene DSP mutation, resulting in arrhythmias, heart failure, and sudden cardiac death. Cardiac MRI typically presents with ring-like subepicardial late gadolinium enhancement which can be mistaken for myocarditis or fatty replacement.
PMID:41796267 | DOI:10.1007/s10554-026-03670-4