Praxis (Bern 1994). 2025 Dec;114(12):434-437. doi: 10.23785/PRAXIS.2025.12.007.
ABSTRACT
Schnitzler syndrome is a rare autoinflammatory disease that primarily manifests in adulthood. In cases presenting with chronic urticaria and paraproteinemia, Schnitzler syndrome should be considered in the differential diagnosis, and the Strassburg criteria should be applied to establish the diagnosis. IL-1 inhibitors have proven to be an effective long-term treatment for Schnitzler syndrome. Patients should be moni-tored for the potential development of lymphoproliferative disorders and/or amyloidosis.
PMID:41569244 | DOI:10.23785/PRAXIS.2025.12.007